Radiological· Findings in Mucopolysaccharidosis
Soh a Mohamed Galal El-Tahawy;
Abstract
Mucopolysaccharidosis are a group of lysosomal storage disease, clinically progressive hereditary disorders of MPs metabolism characterized by accumelation of glycosaminoglycans in various tissues resulting in a wide varity of skeletal, visceral and mental abnormalities.
This study included 10 patients having MPs skull x-ray, x ray cervical spine, x-ray dorsolumber spine, CT brain, CT cervical spine was done to all cases and positive data was studied, 6 patients were having brain atrophy, 3 cases were having adontoid hypoplasia, 4 cases were having white matter low density and only 2 cases were having spinal cord compressi On.
This study included 10 patients having MPs skull x-ray, x ray cervical spine, x-ray dorsolumber spine, CT brain, CT cervical spine was done to all cases and positive data was studied, 6 patients were having brain atrophy, 3 cases were having adontoid hypoplasia, 4 cases were having white matter low density and only 2 cases were having spinal cord compressi On.
Other data
| Title | Radiological· Findings in Mucopolysaccharidosis | Other Titles | اكتشاف الاشعة التشخيصية في مرض عديدات التسكر المخاطيىة | Authors | Soh a Mohamed Galal El-Tahawy | Keywords | Mucopolysccharidosis. - Dysostosis multiplex. - Odontoidhypoplasia. - Low density white matter. - J Shaped sella. - Atlanto axial sublaxation. - Spinal cord compression | Issue Date | 2001 |
Attached Files
| File | Size | Format | |
|---|---|---|---|
| Soha Mohamed Galal El-Tahawy.pdf | 2.11 MB | Adobe PDF | View/Open |
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